World Journal of Case Reports

Case Report | Open Access

Volume 2022 - 1 | Article ID 211 | http://dx.doi.org/10.51521/WJCRCI.2022.1207

A Case of Recurrent Kikuchi-Fujimoto Disease

Academic Editor: Guangyu Li

  • Received 2022-07-11
  • Revised 2022-08-13
  • Accepted 2022-08-18
  • Published 2022-08-26

ASHAQ PARREY, MURTAZA NOOR, MOHD.ISMAIL, MANZOOR KOKA, MOHD. ASHRAF

 

Ashaq Hussain Parrey, MD Internal medicine GMC Srinagar

Murtaza Noor, MD Internal medicine GMC Srinagar

Mohd. Ismail, MD Internal medicine GMC Srinagar

Manzoor Koka, MD Internal medicine GMC Srinagar

Mohd. Ashraf, MD Internal medicine GMC Srinagar

 

Corresponding Author: Dr.Ashaq Hussain Parrey. M.D Assistant Professor Medicine Government Medical Collage Srinagar India. Email: chogalpora@gmail.com, Ph: +918825014787

 

Citation: Ashaq Parrey, Murtaza Noor, Mohd.Ismail, Manzoor Koka, Mohd. Ashraf (2022) A Case of Recurrent Kikuchi-Fujimoto Disease. World J Case Rep Clin Img. 2022 July-Aug; 1(2):1-4.

 

ABSTRACT

Kikuchi-Fujimoto disease or necrotising histiocytic lymphadenitis is a rare non-malignant immune mediated condition that presents with cervical lymphadenopathy, upper respiratory tract symptoms, low grade fever, night sweats and weight loss in young females. Although mostly self-resolving after months of onset, recurrences have been reported increasingly, with certain specific factors predicting frequent relapse. It closely mimics lymphoproliferative disorders and has been reported as a harbinger of autoimmune diseases like SLE. Here we describe a case of a young female with past history of KD who presented with painful cervical lymphadenopathy, fever, cough, along with leukopenia and splenomegaly with node biopsy revealing KD, who was treated with a prolonged course of steroids for the relapsing disease.

 

Keywords: Kikuchi- Fujimoto disease, Necrotising Histiocytic Lymphadenitis, SLE

 

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